NFIL3-deficient mice develop microbiota-dependent, IL-12/23-driven spontaneous colitis

J Immunol. 2014 Feb 15;192(4):1918-27. doi: 10.4049/jimmunol.1301819. Epub 2014 Jan 17.

Abstract

NFIL3 is a transcription factor that regulates multiple immunologic functions. In myeloid cells, NFIL3 is IL-10 inducible and has a key role as a repressor of IL-12p40 transcription. NFIL3 is a susceptibility gene for the human inflammatory bowel diseases. In this article, we describe spontaneous colitis in Nfil3(-/-) mice. Mice lacking both Nfil3 and Il10 had severe early-onset colitis, suggesting that NFIL3 and IL-10 independently regulate mucosal homeostasis. Lymphocytes were necessary for colitis, because Nfil3/Rag1 double-knockout mice were protected from disease. However, Nfil3/Rag1 double-knockout mice adoptively transferred with wild-type CD4(+) T cells developed severe colitis compared with Rag1(-/-) recipients, suggesting that colitis was linked to defects in innate immune cells. Colitis was abrogated in Nfil3/Il12b double-deficient mice, identifying Il12b dysregulation as a central pathogenic event. Finally, germ-free Nfil3(-/-) mice do not develop colonic inflammation. Thus, NFIL3 is a microbiota-dependent, IL-10-independent regulator of mucosal homeostasis via IL-12p40.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adoptive Transfer
  • Animals
  • Arabidopsis Proteins / biosynthesis
  • Basic-Leucine Zipper Transcription Factors / genetics
  • Basic-Leucine Zipper Transcription Factors / metabolism*
  • Cells, Cultured
  • Colon / immunology
  • Colon / pathology
  • Genetic Predisposition to Disease
  • Inflammatory Bowel Diseases / genetics*
  • Inflammatory Bowel Diseases / microbiology*
  • Interleukin-10 / genetics*
  • Interleukin-12 Subunit p40 / genetics
  • Interleukin-12 Subunit p40 / metabolism*
  • Interleukin-23 Subunit p19 / genetics
  • Interleukin-23 Subunit p19 / metabolism*
  • Membrane Proteins / biosynthesis
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Microbiota / immunology*
  • Th1 Cells / immunology
  • Th17 Cells / immunology
  • Tumor Necrosis Factor-alpha / genetics

Substances

  • Arabidopsis Proteins
  • Basic-Leucine Zipper Transcription Factors
  • IL10 protein, mouse
  • Il23a protein, mouse
  • Interleukin-12 Subunit p40
  • Interleukin-23 Subunit p19
  • Membrane Proteins
  • Nfil3 protein, mouse
  • Rma1 protein, Arabidopsis
  • Tumor Necrosis Factor-alpha
  • Interleukin-10